Korean Journal of Anesthesiology

The Korean Society of Anesthesiologists (대한마취통증의학회)
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Fiberoptic Bronchoscopic Intubation in a Patient with Treacher-Collins Syndrome

굴곡성 기관지경을 이용한 Treacher-Collins 증후군 환아의 기관내 삽관

Kim, Yoon-Hee;Lee, Jung-Zoo;Yun, Seok-Hwa;Lee, Jeong-Un
김윤희;이정주;윤석화;이정은

  • Published : 20020600
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Abstract

The Treacher-Collins syndrome is a rare congenital anomaly characterized by mandibular, maxillary, and malar bone hypoplasia, bilateral deformities of auricles, lower lid defects, and antimongoloid slant of the palpebral fissures. The syndrome is associated with considerable difficulty in airway management during anesthesia; difficult, often impossible, endotracheal intubation and face mask ventilation. We report case of Treacher-Collins syndrome in 13-year-old girl who was intubated with fiberoptic bronchoscope and discuss anesthetic consideration.

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References

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