Korean Journal of Otorhinolaryngology-Head and Neck Surgery

Korean Society of Otolaryngology-Head and Neck Surgery (대한이비인후과학회)
권호 표지

A Case of Hereditary Hemorrhagic Telangiectasia Managed withIntranasal Topical Estrogen

비강내 국소 에스트로겐으로 치료한 유전성 출혈성모세혈관확장증 1예

Song, Jeong-Hwan;Kim, Hyeon-Jun;Yun, Yong-Ro;Kim, Yun-Tae
송정환;김현준;윤용로;김윤태

  • Published : 20060000
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Abstract

Hereditary hemorrhagic telangiectasia is an autosomal dominant disorder affecting blood vessels of the skin, mucous membrane and viscera. It is characterized by a clinical triad of multiple telangiectasia, recurrent hemorrhages and familial occurrence. In 80% of patients, epistaxia is the first presenting symptom. It can have a massive impact on the quality of life of those affected. Otolaryngologists should be familiar with this disease because of its potential systemic complication. Recently, we have experienced a 69 year old female complaining of melena and recurrent epistaxis for 20 years. Epistaxis was successfully managed with topical estrogen ointment.

Keywords

References

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