Clinical and Molecular Hepatology (대한간학회지)

The Korean Association for the Study of the Liver (대한간학회)
권호 표지

A case of hepatic epithelioid hemangioendothelioma that caused extrahepatic metastases without intrahepatic recurrence after hepatic resection

간절제술 후 원발병소인 간내 재발 없이 간외전이를 일으킨 간상피모양혈관내피종 1예

Jeong, Soung-Won;Woo, Hyun-Young;You, Chan-Ran;Huh, Won-Hang;Bae, Si-Hyun;Choi, Jong-Young;Yoon, Seung-Kew;Jung, Chan-Kwon;Jung, Eun-Sun
정승원;우현영;유찬란;허원행;배시현;최종영;윤승규;정찬권;정은선

  • Published : 20080000
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Abstract

Epithelioid hemangioendothelioma is a neoplasm of vascular origin with a low-to-intermediate malignant potential and is one of the rare sarcomas arising from the liver. Its etiology is unknown and its clinical outcome is unpredictable. There is no generally accepted therapeutic strategy because of its rarity and the variable natural course between hemangioma and angiosarcoma. We report a case of a 64-year old woman who underwent hepatic resection due to epithelioid hemangioendothelioma in the right lobe that progressed to extrahepatic metastases of the bone, pleura, and peritoneum 22 months later. However, after resection there was no primary hepatic recurrence. (Korean J Hepatol 2008;14:525-531)

간상피모양혈관내피종은 혈관에서 기원하는 종양으로 간에서 발생하는 가장 드문 육종 중의 하나로서 저등도에서 중등도의 악성도를 가지고 있다. 아직까지 원인은 알려져 있지 않으며 예후 또한 예측하기 어렵다. 발생빈도가 낮고, 불균일한 특성, 다양한 임상경과 등으로 현재까지 정해져 있는 치료지침은 없다. 저자들은 64세 여자 환자에서 우엽에 발생한 간상피모양혈관내피종을 간절제술을 시행하고 22개월 후에, 원발병소인 간내 재발은 없이 골, 흉막, 복강 등으로 간외전이를 보인 사례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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